Pulmonary nodules and primary Sjögren syndrome: a case report

Pulmonary nodules and primary Sjögren syndrome: a case report

Authors

  • Sofia Rigoni Università degli studi di Parma
  • Anna Lanati University of Parma
  • Francesco Cirimele University of Parma
  • Alfredo Antonio Chetta University of Parma

Keywords:

Primary Sjögren syndrome, pulmonary nodules, lymphoma

Abstract

Primary Sjögren syndrome (pSS) is a systemic autoimmune disorder that principally affects the exocrine glands but can also affect systemic or extra-glandular sites. Approximately 65-80% of patients with Sjogren's demonstrate pulmonary involvement at the CT scan and pulmonary nodules (PNs) can be encountered as a common finding.

We present the case of a 49-year-old woman admitted to the emergency department for chest pain and fever. The patient was diagnosed with pSS fourteen years prior and had never taken therapy or followed regular check-ups. At the HRTC were found PNs that were studied trough a CT-PET and a needle biopsy via CT guidance, which showed diffuse large B cell lymphoma.

This case report underlies the importance of check-ups and the need for a multidisciplinary approach in the care of Sjögren’s syndrome patients.

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Published

05-12-2023

Issue

Section

CASE REPORTS

How to Cite

1.
Rigoni S, Lanati A, Cirimele F, Chetta AA. Pulmonary nodules and primary Sjögren syndrome: a case report. Acta Biomed [Internet]. 2023 Dec. 5 [cited 2024 Oct. 11];94(6):e2023261. Available from: https://www.mattioli1885journals.com/index.php/actabiomedica/article/view/15184