Pulmonary arterial hypertension in childhood: an unsual presentation with fibrosing mediastinitis

Pulmonary arterial hypertension in childhood: an unsual presentation with fibrosing mediastinitis

Authors

  • Elisabetta Teopompi University Hospital of Parma
  • Bertrand Tchana University Hospital of Parma
  • Alfredo Chetta University Hospital of Parma
  • Marina Aiello University Hospital of Parma
  • Marta Sgrignoli University Hospital of Parma
  • Nicola Carano University Hospital of Parma
  • Aldo Agnetti University Hospital of Parma

Keywords:

pulmonary hypertension, pulmonary veins, heart failure, respiratory failure

Abstract

Acquired stenosis of normally connected pulmonary veins is a rare condition in children, usually associated with mediastinal processes. It may present later with a less specific clinical picture, symptoms and signs mimicking chronic lung disease. Fibrosing mediastinitis is a rarer disorder of unknown etiology, although several suspected causes such as granulomatous diseases, characterized by fibrous tissue proliferation within the mediastinum, leading to respiratory and cardiac failure by bronchial obstruction or pulmonary hypertension.

Author Biographies

Elisabetta Teopompi, University Hospital of Parma

Department of Clinical and Experimental Medicine, Section of Respiratory Disease

Bertrand Tchana, University Hospital of Parma

Department of Pediatrics, Pediatric Cardiology Unit

Alfredo Chetta, University Hospital of Parma

Department of Clinical and Experimental Medicine, Section of Respiratory Disease

Marina Aiello, University Hospital of Parma

Department of Clinical and Experimental Medicine, Section of Respiratory Disease

Marta Sgrignoli, University Hospital of Parma

Department of Pediatrics

Pediatric cardiology Unit

Nicola Carano, University Hospital of Parma

Department of Pediatrics

Pediatric Cardiology Unit

Aldo Agnetti, University Hospital of Parma

Department of Pediatrics

Pediatric Cardiology Unit

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Published

09-05-2014

How to Cite

1.
Pulmonary arterial hypertension in childhood: an unsual presentation with fibrosing mediastinitis. Acta Biomed [Internet]. 2014 May 9 [cited 2024 May 22];85(1):68-72. Available from: https://www.mattioli1885journals.com/index.php/actabiomedica/article/view/3005

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