An unusual cause of Steven-Johnson Syndrome
Authors
-
Claudia De Guido
Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
-
Adriana Calderaro
Department of Medicine and Surgery, University of Parma, Parma, Italy
-
Maria Beatrice Ruozi
Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
-
Valentina Maffini
Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
-
Margherita Varini
Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
-
Irene Lapetina
Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
-
Monica Rubini
Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
-
Sara Montecchini
Department of Medicine and Surgery, University of Parma, Parma, Italy
-
Carlo Caffarelli
Clinica Pediatrica, Department of Medicine and Surgery, University of Parma, Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
-
Icilio Dodi
Children Hospital “P. Barilla”, Azienda Ospedaliero-Universitaria, Parma University Hospital, Parma, Italy
Keywords:
Steven-Johnson Syndrome, allergy, enterovirus, corticosteroids, cyslosporine A
Abstract
SJS is a rare mucocutaneous syndrome characterized by skin and mucous detachment. The main etiological factors are drugs and infections; sometimes the cause remains unknown. In the prodromal phase we observed non-specific symptoms, followed by mucocutaneous manifestation. Due to risk of complications and mortality a multidisciplinary approach is needed. We present a case of a girl with an atypical presentation of SJS related to Enterovirus.
License
This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Transfer of Copyright and Permission to Reproduce Parts of Published Papers.
Authors retain the copyright for their published work. No formal permission will be required to reproduce parts (tables or illustrations) of published papers, provided the source is quoted appropriately and reproduction has no commercial intent. Reproductions with commercial intent will require written permission and payment of royalties.
How to Cite
1.
De Guido C, Calderaro A, Ruozi MB, et al. An unusual cause of Steven-Johnson Syndrome.
Acta Biomed. 2020;91(1):128-131. doi:
10.23750/abm.v91i1.7692